Recent
Hematology/Oncology Faculty Publications (2010-2011)
JOURNAL ARTICLES:
1.
Agrawal AK,
Chang PP, Feusner J. Twice
weekly Pneumocystis jiroveci pneumonia prophylaxis with
trimethoprim-sulfamethoxazole in pediatric patients with acute lymphoblastic
leukemia. J Pediatr Hematol Oncol. 2010;33:e1-4.
2.
Agrawal AK, Haddad FG, Matsunaga
A. Acute nonimmune hemolytic anemia without fulminant
hepatitis in
3.
4.
5.
Ballas
SK, Lieff S, Benjamin LJ, Dampier CD, Heeney MM, Hoppe C, Johnson CS,
Rogers ZR, Smith-Whitley K, Wang WC, Telen MJ.
Definitions of the phenotypic manifestations of sickle cell disease.
Am J Hematol. 2010;85:6-13.
6.
Bloch E, Herwaldt B, Hagar RW. A third described case of transfusion-transmitted babesia
duncani: an additional consideration following transfusion. Transfusion. 2011
(submitted).
7.
Buchanan
G, Vichinsky E, Krishnamurti L, Shenoy S. Severe sickle cell
disease--Pathophysiology and therapy. Biol Blood Marrow Transplant. 2010;16:S64-67.
8.
Chang
P, Kang M, Xiao A, Chang J, Feusner J, Buffler P, Wiemels J. FLT3 mutation incidence and timing of
origin in a population case series of pediatric leukemia.
9.
Cooper
TM, Franklin J, Gerbing RB, Alonzo TA, Hurwitz C, Raimondi SC, Hirsch B, Smith
FO, Mathew P, Arceci RJ, Feusner J, Iannone R, Lavey RS, Meshinchi S,
Gamis A. AAML03P1, a pilot study of
the safety of gemtuzumab ozogamicin in combination with chemotherapy for newly
diagnosed childhood acute myeloid leukemia: A report from the children's
oncology group. Cancer. 2011.
10.
Dampier
C, Lieff S, LeBeau P, Rhee S, McMurray M, Rogers Z, Smith-Whitley K, Wang W.
Comprehensive Sickle Cell Centers (
11.
DeBaun
M, Frei-Jones M, Vichinsky E. Hemoglobinopathies. In:
Kliegman R, ed. Nelson Textbook of Pediatrics (ed
19th).
12.
Di
Marco V, Capra M, Angelucci E, Borgna-Pignatti C, Telfer P, Harmatz P,
Kattamis A, Prossamariti L, Filosa A, Rund D, Gamberini MR, Cianciulli P, De Montalembert
M, Gagliardotto F, Foster G, Grange JD, Cassara F, Iacono A, Cappellini MD,
Brittenham GM, Prati D, Pietrangelo A, Craxi A, Maggio A. Management of chronic viral hepatitis in
patients with thalassemia: recommendations from an international panel. Blood.
2010;116:2875-2883.
13.
Fung EB. Nutritional deficiencies in patients with
thalassemia. Ann N Y Acad Sci. 2010;1202:188-196.
14.
Fung EB,
Aguilar C, Micaily I, Haines D, Lal A.
Treatment of vitamin D deficiency in transfusion-dependent
thalassemia. Am J Hematol. 2011.
15.
Fung EB, Vichinsky
EP, Kwiatkowski JL, Huang J, Bachrach LK, Sawyer AJ, Zemel BS. Characterization of low bone mass in young patients with
thalassemia by DXA, pQCT and markers of bone turnover. Bone. 2011;48:1305-1312.
16.
Fung EB, Xu
Y, Kwiatkowski JL, Vogiatzi MG, Neufeld E, Olivieri N, Vichinsky EP,
Giardina PJ. Thalassemia Clinical Research Network. Relationship between chronic
transfusion therapy and body composition in subjects with thalassemia. J
Pediatr. 2010;157:641-647, 647 e641-642.
17.
Fung EB, Xu
Y, Trachtenberg F, Olivieri N, Kwiatkowski J, Thompson A, Neufeld E, Boudreaux
J, Quinn C, Vichinsky E. Thalassemia Clinical Research Network.
Inadequacy of dietary intake
increases with age in patients with thalassemia. Journal of the American
Diabetic Association. 2011 (accepted with revisions).
18.
Gabrovsky
A, Aderinto A, Spevak M, Vichinsky E, Resar LM. Low dose, oral epsilon aminocaproic acid
for renal papillary necrosis and massive hemorrhage in hemoglobin SC disease.
Pediatr Blood Cancer. 2010;54:148-150.
19.
Gladwin
MT, Barst RJ, Castro OL, Gordeuk VR, Hillery CA, Kato GJ, Kim-Shapiro DB,
Machado R, Morris CR, Steinberg MH, Vichinsky EP. Pulmonary hypertension and NO in sickle
cell. Blood. 2010;116:852-854.
20.
Gladwin
MT, Kato GJ, Weiner D, Onyekwere OC, Dampier C, Hsu L, Hagar RW, Howard
T, Nuss R, Okam MM, Tremonti CK, Berman B, Villella A, Krishnamurti L, Lanzkron
S, Castro O, Gordeuk VR, Coles WA, Peters-Lawrence M, Nichols J, Hall MK,
Hildesheim M, Blackwelder WC, Baldassarre J, Casella JF. Nitric oxide for inhalation in the acute
treatment of sickle cell pain crisis: a randomized controlled trial. JAMA.
2011;305:893-902.
21.
Gold
JI, Treadwell M, Weissman L, Vichinsky E. The mediating effects of family
functioning on psychosocial outcomes in healthy siblings of children with
sickle cell disease. Pediatr Blood Cancer. 2011.
22.
Gyang E, Yeom K, Hoppe C, Partap
S, Jeng M. Effect of chronic red cell
transfusion therapy on vasculopathies and silent infarcts in patients with
sickle cell disease.
Am J Hematol. 2011;86:104-106.
23.
Hazen
RA, Eder M, Drotar D, Zyzanski S, Reynolds AE, Reynolds CP, Kodish E, Noll RB, Feusner
(collaborator) J. A
feasibility trial of a video intervention to improve informed consent for
parents of children with leukemia. Pediatric Blood & Cancer. 2010;55:113-118.
24.
Hoppe C, Kuypers
F, Larkin S, Hagar W, Vichinsky E, Styles L. A pilot study of the short-term use of
simvastatin in sickle cell disease: effects on markers of vascular dysfunction.
Br J Haematol. 2011;153:655-663.
25.
Hue-Roye
K, Hipsky CH, Velliquette RW, Fuchisawa A, Lomas-Francis C, Hoppe C,
Reid ME. A novel RHCE*ce 48C, 733G allele with Nucleotide 941C in Exon 7 encodes
an altered red blood cell e antigen. Transfusion. 2010;51:32-35.
26.
Hung
K, Killilea D, Firnkes S, Ory D, Volitakis I, Hastings C, Bush A. NPC1 modulates metal homeostasis: a
metallomic analysis. Metallomics (submitted, May 2011). 2011.
27.
Jacobs JE, Hastings
C. Isolated extramedullary
relapse in childhood acute lymphocytic leukemia. Curr Hematol Malig Rep.
2010;5:185-191.
28.
Jacobs
JE, Quirolo K, Vichinsky E.
Novel influenza A (H1N1) viral infection in pediatric patients with
sickle-cell disease. Pediatr Blood Cancer. 2011;56:95-98.
29.
James
EB, Vreman HJ, Wong RJ, Stevenson DK, Vichinsky E, Schumacher L, Hall
JY, Simon J, Golden DW, Harmatz P.
Elevated exhaled carbon monoxide concentration in hemoglobinopathies
and its relation to red blood cell transfusion therapy. Pediatr Hematol
Oncol. 2010;27:112-121.
30.
Johnson
RM, Ho YS, Yu DY, Kuypers FA, Ravindranath Y, Goyette GW. The effects of disruption of genes for
peroxiredoxin-2, glutathione peroxidase-1, and catalase on erythrocyte
oxidative metabolism. Free Radic Biol Med. 2010;48:519-525.
31.
Kanathezhath B,
Hazard FK, Guo H, Kidd J, Azimi M, Kuypers FA, Vichinsky EP, Lal
A. Hemoglobin Hakkari: an
autosomal dominant form of beta thalassemia with inclusion bodies arising from
de novo mutation in exon 2 of beta globin gene. Pediatr Blood Cancer.
2010;54:332-335.
32.
Kanathezhath B,
Mizokami M, Stanislaus S, Hounshell C, Neumayr L, Guo H, Hearst JE, Walters
MC, Kuypers FA. Improved
engraftment with minimal graft-versus-host disease after major
histocompatibility complex-mismatched cord blood transplantation with
photochemically treated donor lymphocytes. Exp Biol Med (
33.
Kanathezhath B,
Shah A, Secola R, Hudes M, Feusner JH.
The utility of routine surveillance blood cultures in asymptomatic
hematopoietic stem cell transplant patients. J Pediatr Hematol Oncol.
2010;32:327-331.
34.
Kanathezhath B,
Walters MC. Umbilical cord
blood transplantation for thalassemia major. Hematol Oncol Clin North Am.
2010;24:1165-1177.
35.
Kidd JL, Azimi M, Lubin B, Vichinsky
E, Hoppe C. Application of an expanded multiplex
genotyping assay for the simultaneous detection of Hemoglobin Constant Spring
and common deletional alpha-thalassemia mutations. Int J Lab Hematol. 2010;32:373-380.
36.
Klings
E, Machado R, Barst R, Morris CR, Mubarak K, Gordeuk VR, Kato GJ, Ataga
K, Gibbs JS, Castro O, Berman-Rosenzweig E, Sood N, Hsu L, Wilson KC, Telen M,
DeCastro L, Krishnamurti L, Steinberg M, Badesch DB, Gladwin MT. Consensus-based guidelines for the
diagnosis and treatment of pulmonary hypertension of sickle cell disease. Am J Respir Crit Care Med. 2011 (under review).
37.
Kutny MA, Moser B, Laumann K, Feusner
J. FLT mutation status is a predictor of early death in
pediatric acute promyelocytic leukemia: a report from the Children's Oncology
Group. 2011 (submitted).
38.
Kwiatkowski
JL, Yim E, Miller S, Adams RJ, STOP II Study Investigators (E. Vichinsky
collaborator). Effect of transfusion
therapy on transcranial Doppler ultrasonography velocities in children with
sickle cell disease. Pediatr Blood Cancer. 2011;56:777-782.
39.
Lal A, Ames
BN. Association of chromosome damage
detected as micronuclei with hematological diseases and micronutrient status.
Mutagenesis. 2011;26:57-62.
40.
Lal A,
Goldrich ML, Haines DA, Azimi M, Singer ST, Vichinsky EP. Heterogeneity of hemoglobin H disease in
childhood. N Engl J Med. 2011;364:710-718.
41.
Lee
WC, Rigante S, Pisano AP, Kuypers FA.
Large-scale arrays of picolitre chambers for single-cell analysis of
large cell populations. Lab Chip. 2010;10:2952-2958.
42.
Machado
RF, Barst RJ, Yovetich NA, Hassell KL, Kato GJ, Gordeuk VR, Gibbs JS, Little
JA, Schraufnagel DE, Krishnamurti L, Girgis RE, Morris CR, Rosenzweig
EB, Badesch DB, Lanzkron S, Onyekwere O, Castro OL, Sachdev V, Waclawiw MA,
Woolson R, Goldsmith JC, Gladwin MT. Hospitalization
for pain in patients with sickle cell disease treated with sildenafil for
elevated
43.
MacMillan ML, Walters MC,
Gluckman E. Transplant outcomes in bone marrow
failure syndromes and hemoglobinopathies. Semin Hematol. 2010;47:37-45.
44.
Maggio
A, Filosa A, Vitrano A, Aloj G, Kattamis A, Ceci A, Fucharoen S, Cianciulli P,
Grady RW, Prossomariti L, Porter JB, Iacono A, Cappellini MD, Bonifazi F,
Cassara F, Harmatz P, Wood J, Gluud C.
Iron chelation therapy in thalassemia major: A systematic review with
meta-analyses of 1520 patients included on randomized clinical trials. Blood
Cells Mol Dis. 2011.
45.
Mansour
KM, Kuypers FA, Wang TN, Miller AM, Larkin SK, Morris CR. Secretory phospholipase A(2):
a marker of infection in febrile children presenting to a pediatric ED. Am
J Emerg Med. 2010.
46.
Morris CR. Role of Arginase in Sickle Cell Lung
Disease and Hemolytic Anemias. The Open Nitric Oxide Journal. 2010;
47. Morris CR.
Vascular risk assessment in patients with sickle cell disease. Haematologica.
2011;96:1-5.
48.
Morris CR,
Kim H-Y, Trachtenberg F, Wood J, Quinn CT, Sweeters N, Kwiatkowski JL, Thompson
AA, Giardina PJ, Boudreaux J, Olivieri NF, Porter JB, Neufeld EJ, Vichinsky
EP. Risks factors and mortality
associated with an elevated tricuspid-regurgitant-jet-velocity measured by
Doppler-echocardiography in thalassemia: a Thalassemia Clinical Research
Network report. Blood.
2011.
49.
Morris CR, Vichinsky
EP. Pulmonary hypertension in
thalassemia. Ann N Y Acad Sci. 2010;1202:205-213.
50.
Moyer
JD, Nowak RB, Kim NE, Larkin SK, Peters LL, Hartwig J, Kuypers FA,
Fowler VM. Tropomodulin 1-null mice
have a mild spherocytic elliptocytosis with appearance of tropomodulin 3 in red
blood cells and disruption of the membrane skeleton. Blood. 2010;116:2590-2599.
51.
Neumayr L,
Pringle S, Giles S, Quirolo KC, Paulukonis S, Vichinsky EP, Treadwell
MJ. Chart Card: feasibility of a
tool for improving emergency department care in sickle cell disease. J
Natl Med Assoc. 2010;102:1017-1023.
52.
Newaskar
M, Hardy KA, Morris CR. Asthma
in sickle cell disease. ScientificWorldJournal. 2011;11:1138-1152.
53.
54.
Olivieri
NF, Saunthararajah Y, Thayalasuthan V, Kwiatkowski J, Ware RE, Kuypers FA,
Kim HY, Trachtenberg FL, Vichinsky EP. Thalassemia Clinical Research
Network. A pilot study of
subcutaneous decitabine in Beta-thalassemia intermedia. Blood. 2011;118:2708-2711.
55.
Pakbaz
Z, Treadwell M, Kim HY, Trachtenberg F, Parmar N, Kwiatkowski JL,
Cunningham MJ, Martin M, Sweeters N, Neufeld EJ, Giardina PJ, Olivieri N,
Yamashita RC, Vichinsky E. Education
and employment status of children and adults with thalassemia in North America.
Pediatr Blood Cancer. 2010;55:678-683.
56.
Powell
BL, Moser B, Stock W, Gallagher RE, Willman CL, Stone RM, Rowe JM, Coutre S, Feusner
JH, Gregory J, Couban S, Appelbaum FR, Tallman MS, Larson RA. Arsenic trioxide improves event-free and
overall survival for adults with acute promyelocytic leukemia: North American
Leukemia Intergroup Study C9710. Blood. 2010;116:3751-3757.
57.
Quinn
CT, Johnson VL, Kim HY, Trachtenberg F, Vogiatzi MG, Kwiatkowski JL, Neufeld
EJ, Fung E, Oliveri N, Kirby M, Giardina PJ. Thalassemia Clinical
Research Network (E.
Vichinsky collaborator). Renal dysfunction in patients with
thalassaemia. Br J Haematol. 2011;153:111-117.
58.
Quinn
CT, Stuart MJ, Kesler K, Ataga KI, Wang WC, Styles L, Smith-Whitley K, Wun T,
Raj A, Hsu LL, Krishnan S, Kuypers FA, Setty Y, Rhee S, Key NS, Buchanan
GR, (E. Vichinsky collaborator). Tapered oral dexamethasone for the acute
chest syndrome of sickle cell disease. Br J Haematol. 2011.
59.
Quirolo K. How do I transfuse patients with sickle cell
disease? Transfusion. 2010;50:1881-1886.
60.
Rienhoff
HY, Jr., Viprakasit V, Tay L, Harmatz P, Vichinsky E, Chirnomas
D, Kwiatkowski JL, Tapper A, Kramer W, Porter JB, Neufeld EJ. A phase 1 dose-escalation study: safety,
tolerability, and pharmacokinetics of FBS0701, a novel oral iron chelator for
the treatment of transfusional iron overload. Haematologica. 2011;96:521-525.
61.
Ruggeri
A, Eapen M, Scaravadou A, Cairo MS, Bhatia M, Kurtzberg J, Wingard JR, Fasth A,
Lo Nigro L, Ayas M, Purtill D, Boudjedir K, Chaves W, Walters MC, Wagner
J, Gluckman E, Rocha V. Umbilical
cord blood transplantation for children with thalassemia and sickle cell
disease. Biol Blood Marrow Transplant. 2011;17:1375-1382.
62.
Sabloff
M, Chandy M, Wang Z, Logan BR, Ghavamzadeh A, Li CK, Irfan SM, Bredeson CN,
Cowan MJ, Gale RP, Hale GA, Horan J, Hongeng S, Eapen M, Walters MC. HLA-matched sibling bone marrow
transplantation for beta-thalassemia major. Blood. 2010;117:1745-1750.
63.
Sachdev
V, Kato GJ, Gibbs JS, Barst RJ, Machado RF, Nouraie M, Hassell KL, Little JA,
Schraufnagel DE, Krishnamurti L, Novelli EM, Girgis RE, Morris CR,
Rosenzweig EB, Badesch DB, Lanzkron S, Castro OL, Taylor JGt, Hannoush H,
Goldsmith JC, Gladwin MT, Gordeuk VR. Echocardiographic
Markers of Elevated Pulmonary Pressure and Left Ventricular Diastolic
Dysfunction Are Associated With Exercise Intolerance in Adults and Adolescents
With Homozygous Sickle Cell Anemia in the
64.
Satter EK, Walters MC, Hurt M,
Bolton JG, Dever T. A brief overview of the most common
histiocytic disorders.
G Ital Dermatol Venereol. 2010;145:717-731.
65.
Shepherd
JA, Fan B, Lu Y, Marquez L, Salama K, Hwang J, Fung EB. Dual-energy X-ray absorptiometry with
serum ferritin predicts liver iron concentration and changes in concentration
better than ferritin alone. J Clin Densitom. 2010;13:399-406.
66.
Singer ST,
Sweeters N, Vega O, Higa A, Vichinsky E, Cedars M. Fertility potential in thalassemia major
women: current findings and future diagnostic tools. Ann N Y Acad Sci.
2010;1202:226-230.
67.
Singer ST, Vichinsky
EP, Gildengorin G, van Disseldorp J, Rosen M, Cedars MI. Reproductive capacity in iron overloaded women with
thalassemia major.
Blood. 2011;118(10):2878-81.
68.
Singer ST, Vichinsky
EP, Sweeters N, Rachmilewitz E. Darbepoetin
alfa for the treatment of anaemia in alpha- or beta- thalassaemia intermedia
syndromes. Br J Haematol. 2011;Jul;154(2):281-4.
69.
Smith
WR, Ballas SK, McCarthy WF, Bauserman RL, Swerdlow PS, Steinberg MH, Waclawiw
MA. Investigators of the Multicenter Study of Hydroxyurea in Sickle Cell Anemia
(E. Vichinsky collaborator). The association between hydroxyurea
treatment and pain intensity, analgesic use, and utilization in ambulatory
sickle cell anemia patients. Pain Med.
2011; May;12(5):697-705.
70.
Sobota
A, Yamashita R, Xu Y, Trachtenberg F, Kohlbry P, Kleinert DA, Giardina PJ,
Kwiatkowski JL, Foote D, Thayalasuthan V, Porter JB, Thompson AA, Schilling L,
Quinn CT, Neufeld EJ. Thalassemia Clinical Research Network (E. Vichinsky
collaborator). Quality of
life in thalassemia: a comparison of SF-36 results from the thalassemia
longitudinal cohort to reported literature and the
71.
Sohn
EY, Noetzli LJ,
72.
Soupene
E, Dinh NP, Siliakus M, Kuypers FA.
Activity of the acyl-CoA synthetase ACSL6 isoforms: role of the fatty
acid Gate-domains.
73.
Steinberg
MH, McCarthy WF, Castro O, Ballas SK, Armstrong FD, Smith W, Ataga K, Swerdlow
P, Kutlar A, DeCastro L, Waclawiw MA. Investigators of the Multicenter
Study of Hydroxyurea in Sickle Cell Anemia and MSH Patients' Follow-Up (E.
Vichinsky collaborator). The
risks and benefits of long-term use of hydroxyurea in sickle cell anemia: A
17.5 year follow-up. Am J Hematol. 2010;85:403-408.
74.
Stewart
AK, Shmukler BE, Vandorpe DH, Rivera A, Heneghan JF, Li X, Hsu A, Karpatkin M,
O'Neill AF, Bauer DE, Heeney MM, John K, Kuypers FA, Gallagher PG, Lux
SE, Brugnara C, Westhoff CM, Alper SL. Loss-of-function
and gain-of-function phenotypes of stomatocytosis mutant RhAG F65S. Am J Physiol Cell Physiol. 2011.
75.
Tallman
MS, Kim HT, Montesinos P, Appelbaum FR, de la Serna J, Bennett JM, Deben G,
Bloomfield CD, Gonzalez J, Feusner JH, Gonzalez M, Gallagher R, Miguel
JD, Larson RA, Milone G, Paietta E, Rayon C, Rowe JM, Rivas C, Schiffer CA,
Vellenga E, Shepherd L, Slack JL, Wiernik PH, Willman CL, Sanz MA. Does microgranular variant morphology of
acute promyelocytic leukemia independently predict a less favorable outcome
compared with classical M3
76.
77.
Thompson
AA, Cunningham MJ, Singer ST, Neufeld EJ, Vichinsky E, Yamashita
R, Giardina P, Kim HY, Trachtenberg F, Kwiatkowski JL. Thalassemia Clinical
Research Network. Red cell
alloimmunization in a diverse population of transfused patients with
thalassaemia. Br J Haematol. 2011;153:121-128.
78.
Trachtenberg
F, Vichinsky E, Haines D, Pakbaz Z, Mednick L, Sobota A, Kwiatkowski J,
Thompson AA, Porter J, Coates T, Giardina PJ, Olivieri N, Yamashita R, Neufeld
EJ. Thalassemia Clinical Research Network. Iron chelation adherence to deferoxamine
and deferasirox in thalassemia. Am J Hematol. 2011;86:433-436.
79.
Trachtenberg
F, Foote D, Martin M, Carson S, Coates T, Beams O, Vega O, Merelles-Pulcini M,
Giardina P, Kleinert DA, Kwiatkowski J, Thompson A, Neufeld E, Schilling L, Thayalasuthan
V, Pakbaz Z, Yamashita R. Thalassemia Clinical Research Network (E.
Vichinsky collaborator). Pain
as an emergent issue in thalassemia. Am J Hematol. 2010;May;85(5):367–370.
80.
Treadwell M,
Telfair J, Gibson RW, Johnson S, Osunkwo I.
Transition from pediatric to adult care in sickle cell disease:
establishing evidence-based practice and directions for research. Am J
Hematol. 2011;86:116-120.
81.
Treadwell MJ,
Alkon A, Quirolo KC, Boyce WT. Stress
reactivity as a moderator of family stress, physical and mental health, and
functional impairment for children with sickle cell disease. J Dev Behav
Pediatr. 2010;31:491-497.
82.
Treadwell MJ,
Alkon A, Styles L, Boyce WT. Autonomic
nervous system reactivity: children with and without sickle cell disease. Nurs
Res. 2011;60:197-207.
83.
Trobaugh-Lotrario
AD, Finegold MJ, Feusner JH. Rhabdoid
tumors of the liver: rare, aggressive, and poorly responsive to standard
cytotoxic chemotherapy. Pediatr Blood Cancer. 2011;57:423-428.
84.
Vichinsky E. Complexity of alpha thalassemia: growing
health problem with new approaches to screening, diagnosis, and therapy. Ann
N Y Acad Sci. 2010;1202:180-187.
85.
Vichinsky E,
Bernaudin F, Forni GL, Gardner R, Hassell K, Heeney MM, Inusa B, Kutlar A, Lane
P, Mathias L, Porter J, Tebbi C, Wilson F, Griffel L, Deng W, Giannone V,
Coates T. Long-term safety and
efficacy of deferasirox (Exjade) for up to 5 years in transfusional
iron-overloaded patients with sickle cell disease. Br J Haematol. 2011;154:387-397.
86.
Vichinsky EP,
Neufeld EJ. Preface to Cooley's Anemia: Ninth Symposium. Ann N Y Acad Sci. 2010;1202:ix-x.
87.
Vichinsky EP,
Neumayr LD, Gold JI, Weiner MW, Rule RR, Truran D, Kasten J, Eggleston
B, Kesler K, McMahon L, Orringer EP, Harrington T, Kalinyak K, De Castro LM,
Kutlar A, Rutherford CJ, Johnson C, Bessman JD, Jordan LB, Armstrong FD. Neuropsychological dysfunction and
neuroimaging abnormalities in neurologically intact adults with sickle cell
anemia. JAMA. 2010;303:1823-1831.
88.
Vichinsky EP,
Ohene-Frempong K. Approaches to transfusion therapy
and iron overload in patients with sickle cell disease: results of an
international survey.
Pediatr Hematol Oncol. 2011;28:37-42.
89.
Vichinsky EP,
Ohene-Frempong K, Thein SL, Lobo CL, Inati A, Thompson AA, Smith-Whitley K,
Kwiatkowski JL, Swerdlow PS, Porter JB, Marks PW. Transfusion and chelation practices in
sickle cell disease: a regional perspective. Pediatr Hematol Oncol. 2011;28:124-133.
90.
Wahl S, Gildengorin G, Feusner J. Weekend Delay in Initiation of Chemotherapy for Acute
Lymphoblastic Leukemia (
91.
Wahl
S, Garcia A, Hagar RW, Gildengorin G, Quirolo K, Vichinsky E. Lower
alloimmunization rates in pediatric sickle cell patients on chronic
erythrocytapheresis compared to chronic simple transfusions. Transfusion. 2011 (in review).
92.
Wahl S, Vichinsky
E. Pulmonary hypertension in
hemolytic anemias. F1000 Med Rep. 2010;2.
93.
Walter
PB, Porter J, Evans P, Kwiatkowski J, Neufeld E, Coates T, Giardina P, Grady
RW, Vichinsky E, Olivieri N, Trachtenberg F, Alberti D, Fung EB,
Ames BN, Higa A, Harmatz P. Increased
leukocyte apoptosis in Beta-thalassemia patients. Haematologica.
2011 (under review).
94.
Walters MC,
Hardy K, Edwards S, Adamkiewicz T, Barkovich J, Bernaudin F, Buchanan GR, Bunin
N, Dickerhoff R, Giller R, Haut PR, Horan J, Hsu LL, Kamani N, Levine JE,
Margolis D, Ohene-Frempong K, Patience M, Redding-Lallinger R, Roberts IA,
Rogers ZR, Sanders JE, Scott JP, Sullivan KM.
Pulmonary, gonadal, and central nervous system status after bone
marrow transplantation for sickle cell disease. Biol Blood Marrow
Transplant. 2010;16:263-272.
95.
Wang
W, Brugnara C, Snyder C, Wynn L, Rogers Z, Kalinyak K, Brown C, Qureshi A,
Bigelow C, Neumayr L, Smith-Whitley K, Chui DH, Delahunty M, Woolson R,
Steinberg M, Telen M, Kesler K. The
effects of hydroxycarbamide and magnesium on haemoglobin SC disease: results of
the multi-centre CHAMPS trial (E.
Vichinsky collaborator). Br J Haematol. 2011;152:771-776.
96.
Wang
ZJ, Fischer R, Chu Z, Mahoney DH, Jr., Mueller BU, Muthupillai R, James EB,
Krishnamurthy R, Chung T, Padua E, Vichinsky E, Harmatz P. Assessment of cardiac iron by
97.
Wood
JC, Glynos T, Thompson A, Giardina P, Harmatz P, Kang BP, Paley C,
Coates TD. Follow-up report on the
2-year cardiac data from a deferasirox monotherapy trial. Am J Hematol.
2010;85:818-819.
98.
Wood
JC, Glynos T, Thompson A, Giardina P, Harmatz P, Kang BP, Paley C,
Coates TD. Relationship between
labile plasma iron, liver iron concentration and cardiac response in a
deferasirox monotherapy trial. Haematologica. 2011;96:1055-1058.
99.
Wood
JC, Kang BP, Thompson A, Giardina P, Harmatz P, Glynos T, Paley C,
Coates TD. The effect of deferasirox
on cardiac iron in thalassemia major: impact of total body iron stores. Blood.
2010;116:537-543.
100.Zohdi TI, Kuypers
FA, Lee WC. Estimation of red blood cell volume fraction
from overall permittivity measurements. International Journal of Engineering Science. 2011;48:1681-1691.
EDITED BOOKS:
1. Vichinsky
E, Neufeld E eds. Cooley's
Anemia: Ninth Symposium. Annals of the
BOOK CHAPTERS:
1. Ataga K, Vichinsky E. Thrombotic complications in sickle cell disease. In: Aird W,
Bennett JM, Schulman S, White G, eds. Hemostasis
and Thrombosis: Basic Principles and Clinical Practice (ed Sixth (December
2012)): Lippincott Williams & Wilkins; 2011 (in press).
2. DeBaun
M, Frei-Jones M, Vichinsky E. Chapter 456 - Hemoglobinopathies.
In: Kliegman R, ed. Nelson Textbook of Pediatrics (ed
19th): Saunders; 2011.
3. Hagar
W, Morris CR. Adults with Sickle-Cell Disease: Implications of
Increasing Longevity. In: Venkat A, ed. Challenging and Emerging Conditions
in Emergency Medicine: Wiley-Blackwell; 2011:115-140.
4. Hastings C, Agrawal A, Lubin
B, Feusner J. Hematologic supportive care for the child with cancer. In: Pizzo P, Poplack D, eds.
Principles and Practice of Pediatric Oncology (ed Sixth; October 11, 2010): Lippincott
Williams & Wilkins; 2010:1152-1190.
5. Lal
A, Vichinsky E. Sickle Cell Disease. In: Hoffbrand V,
Catovsky D, Tuddenham E, Green ACD, eds. Postgraduate Haematology (ed 6th).
6. Morris CR. Sickle Cell Emergencies. In: Ewen
Amieva-Wang N, ed. A
Practical Guide to Pediatric Emergency Medicine: Caring for Children in the
Emergency Department:
7. Morris
CR, Gladwin MT. Hemolysis-associated pulmonary hypertension in sickle
cell disease and thalassemia. In: Peacock AJ, Naeije R, Rubin LJ, eds.
Pulmonary Circulation (ed 3rd): Hodder Arnold; 2011:728.
8. Morris
CR, Hagar RW. Adults with sickle-cell disease: implications of
increasing longevity. In: Venkat A, ed. Challenging and Emerging Conditions
in Emergency Medicine: Wiley-Blackwell; 2011:376.
EDITORIALS:
1. Walters
MC. Gene therapy and bone marrow
transplantation for thalassemia: changing of the guard? Mol
Ther. 2010;18:1577.
AUDIO/VISUAL MEDIA:
1. Vichinsky
E, Porter J. CancerMinds: Optimizing Chelation Therapy for Pediatric
Iron Overload: Emerging Strategies: ReachMD XM Radio;
LETTERS:
1.
2.
Morris CR. Reduced Global Arginine Bioavailability: A
Common Mechanism of Vasculopathy in SCD and PH. A response to
"Pulmonary hypertension and nitric oxide depletion in sickle cell
disease", Bunn, H. Franklin. Published online
3.
Vichinsky E. Pulmonary hypertension is an important
problem in sickle cell disease. A response to "Pulmonary hypertension
and nitric oxide depletion in sickle cell disease", Bunn, H. Franklin.
Published online
4.
Walters MC,
Sullivan KM. Stem-cell
transplantation for sickle cell disease. N Engl J Med. 2010;362:955-956;
author reply 956.
ABSTRACTS and REVIEWS:
1.
Aguilar
AE, Agrawal AK, Feusner J. Central nervous system relapse in
pediatric acute lymphoblastic leukemia: Should we be making the diagnosis
sooner? American Society of Clinical Oncology (ASCO) Annual Meeting.
2.
Agrawal A,
Saini N, Gildengorin G, Feusner J. Is routine computed tomographic
scanning justified in the early days of persistent febrile neutropenia in
children with malignancies? American Society of Pediatric Hematology
Oncology (ASPHO) 23rd Annual Meeting. Pediatr Blood Cancer 2010; 54(6); poster presentation.
3.
Anurag
K, Agrawal A, Quirolo K, Neumayr L, Flori HR. Rate of
packed red blood cell transfusion in pediatric patients with severe chronic
anemia and normal cardiopulmonary status: how slow is truly necessary? American
Society of Pediatric Hematology Oncology (ASPHO) 23rd Annual Meeting.
Pediatr Blood Cancer 2010; 54(6); poster presentation 122.
4.
Barredo
J, Hastings C, Xiaomin Lea. Inferior outcome with reduced dose
cranial radiation (12 Gy) in isolated
5.
Barst
RJ, Kato GJ, Sachdev V, Nouraie M, Machado RF, Hassell K, Gibbs S, Little J,
Schraufnagel DE, Krishnamurti L, Girgis RE, Morris CR, Badesch DB,
Lanzkron S, Castro O, Rosenzweig EB, Goldsmith JC, Gladwin M, Gordeuk VR. Predictors
of Six-Minute Walk Distance In Adults with Sickle Cell
Anemia In the Walk-PHaSST Study. American Society of Hematology Annual
Meeting.
6.
Chu
J, Guo H, Raphael R, Torkildson J, Vichinsky E, Hastings
C. Disseminated juvenile xanthogranuloma culminating in bone marrow
failure and death. American Society of Pediatric Hematology Oncology
(ASPHO) 24th Annual Meeting.
7.
Detterich
J, Noetzli L, Carson S, Harmatz P, Coates TD, Wood JC. Pulmonary
Hypertension Is Uncommon In Well-Transfused Thalassemia Major Patients. American
Society of Hematology Annual Meeting.
8.
Donthineni
R, Earl J, Neumayr L, Hagar RW, Quirolo KC, Aguilar C, Vichinsky
E. A New Method of Hip Coring Decompression for the Treatment of Femoral
Avascular Necrosis In Sickle Cell Disease:
Perioperative Safety and Preliminary Efficacy Data. American Society of
Hematology Annual Meeting.
9.
Douer
D, Feusner J, et al. Late relapses following All-trans retinoic acid
for Acute Promyelocytic Leukemia are uncommon, respond well to salvage therapy
and occur independently of prognostic factors at diagnosis: Long-term follow-up
of North American Intergroup Study I0129. The 53rd Annual Meeting of the
American Society of Hematology.
10.
Earl
J, Sun P, Martin K, Quirolo K, Vichinsky E, Hoppe C. Evaluation
of Moyamoya Disease in Sickle Cell Anemia Patients After
Encephaloduroarteriosynangiosis. The 53rd Annual Meeting of the American
Society of Hematology.
11.
Feusner JH. Dose-intensified
daunorubicin induction and consolidation plus combined modality maintenance
therapy for children with newly diagnosed acute promyelocytic leukemia (
12.
Freyer
DR, Zung L, Reichman L, Feusner J, Finklestein J, Ruccione K, Gaynon P. Early
decline in left ventricular (
13.
Fung E, Xu
Y, Vichinsky E, Trachtenberg F, Porter J, Neufeld E, Olivieri N, Quinn
C, Kwiatkowski J, Boudreaux J, Odame I, Thompson A. Inadequate Dietary
Intake in Patients with Thalassemia. American Society of Pediatric
Hematology Oncology (ASPHO) 23rd Annual Meeting.
14.
Fung EB,
Kwiatkowski J, Huang J, Gildengorin G, King JC, Vichinsky E. Zinc
Supplementation Improves Bone Density in Patients with Thalassemia. Children's
Hospital Oakland Research Institute Annual Symposium - 50th Anniversary. Award
for outstanding oral presentation.
15.
Fung EB,
Kwiatkowski J, Huang J, Gildengorin G, Vichinsky E, King J. Zinc
Supplementation Improves Bone Density in Patients with Thalassemia. American
Society of Pediatric Hematology/Oncology 23rd Annual Meeting Pediatric
Blood & Cancer (ed Volume 54, Issue 6).
16.
Fung EB,
Reget K, Haines D, Sawyer A, Lal A. Exploring vertebral abnormalities in
patients with thalaseemia and sickle cell disease The 53rd Annual
Meeting of the American Society of Hematology.
17.
Fung EB,
Reget K, Haines D, Sawyer AJ, Lal A. Examing vertebral abnormalities in
patients with hemoglobinopathies. Orthopedic Research Society Annual
Meeting.
18.
Fung EB, Xu
Y, Olivieri N, Giardina P, Porter J, Kwiatkowski J, Odame I, Thompson A,
Neufeld E, Boudreaux J, Quinn C, Trachtenberg F, Vichinsky E, King J. Inadequate
dietery intake in patients with thalassemia. American Society of
Pediatric Hematology/Oncology 23rd Annual Meeting Pediatric Blood &
Cancer (ed Volume 54, Issue 6).
19.
Gallagher
RE, Moser BK, Racevskis J, Poire X, Bloomfield CD, Carroll AJ, Ketterling R,
Ralston D, Schachter-Tokarz E, Zhou D, Chen I-ML, Harvey R, Koval G, Sher DA, Feusner
JH, Tallman MS, Appelbaum FR, Larson RA, Powell BL, Paietta E, Willman CL,
Stock W. Clonal Markers In Relapsed Acute Promyelocytic Leukemia (
20.
Gariepy
C, Lal A, Fung E. Reduced Physical Activity In Adult and
Pediatric Patients with Thalassemia. American Society of Hematology
Annual Meeting.
21.
Giardina
P, Goldberg S, Parkhurst Cain J, Chirnomas D, Esposito J, Paley C, Vichinsky
E. The palatability and tolerability of Deferasirox (EXJADE®) taken with
meals, different liquids, or crushed and added to food. American Society
of Pediatric Hematology Oncology (ASPHO) 24th Annual Meeting.
22.
Goel
R, Hassell K, Castro O, Barst RJ, Rosenzweig EB, Sachdev V, Machado RF, Gibbs
S, Little JA, Schraufnagel DE, Girgis RE, Morris CR, Badesch DB,
Lanzkron S, Goldsmith JC, Gordeuk VR, Kato GJ, Gladwin M, Krishnamurti L. Cigarette
Smoking Is An Independent Predictor of Chronic Pain In Sickle Cell Patients:
Results From the Walk-PHaSST Study. American Society of Hematology
Annual Meeting.
23.
Goldberg
SL, Giardina P, Cain JP, Chirnomas D, Esposito J, Paley CS, Vichinsky E.
The Palatability and Tolerability of Deferasirox (Exjade(R)) Taken with
Meals, Different Liquids, or Crushed and Added to Food. American Society
of Hematology Annual Meeting.
24.
Gonzalez
A, Hagar RW, Hoehner C, Fung E. Liver iron, Vitamin D, and
bone mineralization in sickle cell disease. CHORI Summer Student
Symposium.
25.
Green
NS, Ender K, Pashankar F, Driscoll C, Giardina P, Mullen CA, Clark L, Crotty J,
Burney M, Hoppe C, Barral S. Genetics of HbF and HbF Response to
Hydroxyurea In Pediatric Sickle Cell Disease: A Multi-Site Pilot Analysis of
Candidate SNP Variants. American Society of Hematology Annual Meeting.
26.
Hagar RW. The
burden of sickle cell pain. Sickle Cell Adult Provider Network Annual
Symposium.
27.
Hagar RW. Chronic
renal disease in adult sickle cell patients. 5th Annual Sickle Cell
Disease Research and Educational Symposium and Annual National Sickle Cell
Scientific Meeting.
28.
Hagar RW,
Kurio G, Hoehner C, Earl J, Neumayr L. Cardiac iron in
hypertransfused sickle cell patients. 5th Annual Sickle Cell Disease
Research and Educational Symposium and Annual National Sickle Cell Scientific
Meeting.
29.
Haines
D, Carson S, Green S, Martin M, Coates TD, Vega OO, Gerstenberger E, Braunstein
J, Calamaras D, Dzackova R, Giardina P, Klienert D, Kwiatkowski J, Mendoza TR,
Merelles-Pulcini M, Neufeld EJ, Olivieri NF, Schilling L, Vichinsky E,
Trachtenberg F. Phenomenon of Pain In Thalassemia: A Prospective Analysis by
the Thalassemia Clinical Research Network (TCRN). American Society of
Hematology Annual Meeting.
30.
Hastings C,
Killilea D, Suh J, Browne R. Clinical experience and biomarker assessment
with intravenous and intrathecal infusions of hydroxyl-propyl-beta-cyclodextrin
in identical twin patients with Niemann-Pick Type C Disease. 2011
Scientific Conference on Niemann-Pick Type C Disease. Notre Dame, Indiana;
31.
Hastings C, Torkildson
J, Raphael R. Intrathecal hydroxyl-propyl-beta-cyclodextrix
reverses hearing loss in identifal twin girls with Niemann-Pick Type C Disease.
12th International Congress of Human Genetics/61st Annual Meeting of The American Society of Human Genetics.
32.
Heeney
M, Mueller B, Baltz B, Paley C, Esposito J, Sharma S, Vichinsky E. Baseline
characteristics of patients with sickle cell disease in an ongoing 5-year,
prospective, noninterventional registry trial. The 53rd Annual Meeting
of the American Society of Hematology.
33.
Kanathezhath B, Feusner J. Evaluation
of: [Delaney C et al. Notch-mediated expansion of human cord blood progenitor
cells capable of rapid myeloid reconstitution. Nat Med. 2010 Feb; 16(2):232-6;
doi: 10.1038/nm.2080]. Faculty of 1000. 2010;31 Aug
2010. Http://F1000.com/1821956
34.
Kanathezhath B,
Feusner J. Evaluation of:
[Khorana AA et al. Can literature enhance oncology training? A pilot humanities
curriculum. J Clin Oncol. 2011 Feb 1; 29(4):468-71; doi:
10.1200/JCO.2010.33.3617]. Faculty of 1000. 2011;11 Mar
2011. Http://F1000.com/8865959
35.
Kanathezhath B,
Larkin SK, Kaplan J, Walters MC, Kuypers F. Augmented
Regulatory T Cell Response After Photochemical
Treatment Alleviates Acute Graft-Versus-Host Disease and Improves Survival.
American Society of Hematology Annual Meering.
36.
Kanathezhath B,
Mizokami M, Hounshell C, Neumayr L, Guo H, Walters M, Kuypers
F. Improved hematopoietic engraftment without graft versus host disease
by "add-back" of photochemically treated T lymphocutes in mismatched
cord blood transplantation. The American Society for Blood and Marrow
Transplantation, BMT Tandem Meeting (ed oral
presentation).
37.
Kanathezhath B,
Neumayr L, Guo H, Walters M, Kuypers F. Augmentation Of
Hematopoietic Engraftment Without Graft Versus Host Disease By “Add-Back” Of
Photochemically Treated T Lymphocytes In Mismatched Cord Blood Transplantation.
The American Society for Blood and Marrow Transplantation, BMT Tandem
Meeting. Biology of Blood and Marrow Transplantation (ed
Issue 2, Supplement).
38.
Kanathezhath B,
Stanislaus S, Kaplan J, Larkin S, Kuypers F, Walters M. Augmented
Regulatory T Cell Response After Photochemical Treatment Alleviates Acute
Graft-Versus Host Disease and Improves Survival The American Society for
Blood and Marrow Transplantation, BMT Tandem Meeting. Biology of Blood and
Marrow Transplantation (ed Issue 2, Supplement).
39.
Killilea
D, Suh J, Mattson N, Zetterberg H, Portelius E, Blennow K, Hung Y, Bush A, Hastings
C. Characterization of biomarkers during investigative therapy of
hydroxyl-propyl-beta-cyclodextrin in Niemann-Pick Type C Disease. 12th
International Congress of Human Genetics/61st Annual Meeting of The American Society of Human Genetics.
40.
Klaassen
R, Merells-Pulcini M, Barrowman N, Vichinsky E, Sweeters N, Kirby M,
Neufeld E, Kwiatkowski J, Wu J, Vickars L, Blanchette V, Forgie M, Yamashita R,
Wong-Rieger D, Young N.
41.
Klaassen
R, Vichinsky E, Kirby M, Neufeld E, Kwiatkowski J, Wu J, Vickars L,
Barrowman N, Merelles-Pulcini M, Yamashita R, Wong-Rieger D, Young NL, Sweeters
N. Validation and reliability of a disease-specific quality-of-life measure
(the TranQol) in adults with thalassemia major. International Society
for Quality of Life Research18th Annual Conference.
42.
Kleinert
D, Goldberg S, Parkhurst J, Chimomas D, Esposito J, Paley C, Vichinsky E,
Giardina P. A single-arm, open-label study of the palatability and
tolerability of deferasirox (Exjade) taken with meals, different liquids, or
crushed and added to food. Association of Pediatric Hematology/Oncology
Nurses (APHON) 36th Annual Conference & Exhibit.
43.
Krishnamurti
L, Goel R, Castro O, Barst RJ, Rosenzweig EB, Sachdev V, Machado RF, Gibbs S,
Little JA, Schraufnagel DE, Girgis RE, Morris CR, Badesch DB, Lanzkron
S, Goldsmith JC, Gordeuk VR, Kato GJ, Gladwin M, Hassell K. Chronic Pain Is
An Independent Predictor of Lower 6 Minute Walk Distance In Patients with
Sickle Cell Disease: Results From Walk-PHaSST Study. American Society of
Hematology Annual Meeting.
44.
Kutlar
A, Ataga KI, Reid M, Blair-Britt LA, Vichinsky E, Neumayr L, Labotka RJ,
Glass J, Small-WIlliams A, Keefer J, Shen L, Boosalis MS, Thomson A, Bobbitt P,
Wallis W, Johnson E, Berenson RJ, Perrine SP. Phase 1/2 Clinical Trial of
HQK-1001, An Oral Fetal Hemoglobin Stimulant, In Sickle Cell Anemia. American
Society of Hematology Annual Meeting.
45.
Kutny
MA, Moser BK, Gregory J, Woods WG, Feusner JH, Meshinchi S. FLT3
Mutations Are Prevalent and Are Significantly Associated with Induction Death
In Pediatric Acute Promyelocytic Leukemia, a Report From the Children's
Oncology Group. American Society of Hematology Annual Meeting.
46.
Lal A,
Goldrich ML, Foote D, Azimi M, Singer ST, Vichinsky E. Hemoglobin
H disease during childhood. American Society of Hematology Annual
Meeting.
47.
Lal A,
Goldrich ML, Foote D, Azimi M, Singer ST, Vichinsky E. Longitudinal
Follow-up From Newborn Screening Reveals Deletional Hemoglobin H Disease and
Hemoglobin H Constant Spring Disease Are Distinct Thalassemia Syndromes. American
Society of Hematology Annual Meeting.
48.
Lal A,
Micaily I, Foote D, Fung E. A Simple Regimen to Correct Vitamin D
Deficiency In Transfusion-Dependent Thalassemia with
High-Dose Ergocalciferol. American Society of Hematology Annual Meeting.
49.
Lal A,
Sweeters N, Ng V, Foote D, Evans P, Neumayr L, Kurio G, Harmatz P,
Porter JB, Vichinsky E. Combined Chelation Therapy with Deferasirox
and Deferoxamine In Transfusion-Dependent Thalassemia. American Society
of Hematology Annual Meeting.
50.
Lal A,
Sweeters N, Ng V, Haines D, Neumayr L, Kurio G, Harmatz P,
Evans P, Porter JB, Vichinsky E. Combined Chelation Therapy with
Deferasirox and Deferoxamine In Transfusion-Dependent Thalassemia. 12th
International Conference on Thalassemia.
51.
Machado
RF, Barst RJ, Yovetich NA, Hassell KA, Goldsmith JC, Woolson R, Gordeuk VR,
Gibbs S, Little JA, Kato GJ, Schraufnagel DE, Krishnamurti L, Girgis R, Morris
CR, Berman-Rosenzweig E, Badesch DB, Waclawiw MA, Gladwin MT. Evaluation
of Sildenafil Therapy for Patients with Sickle Cell Disease and Increased
Tricuspid Regurgitant Velocity: Preliminary Results of the Walk-PHaSST Trial.
American Thoracic Society International Conference. Oral Presentation,
[B16] PULMONARY ARTERIAL HYPERTENSION: FROM ASSESSING RISK TO THERAPEUTIC
RESULTS.
52.
Marsh A, Lo
L, Feusner J. Sorafenib (Soraf) and bevacizumab (Beva) for recurrent
metastatic hepatoblastoma (HB). American Society of Clinical Oncology
(ASCO) Annual Meeting.
53.
Mietus-Snyder
M, Jung S, Ames BN, Flores B, Lal A. Metabolic abnormalities in obese
teens may relate to poor diets. American Heart Association Nutrition,
Physical Activity and Metabolism / Cardiovascular Disease Epidemiology and
Prevention and Nutrition, Physical Activity, and Metabolism (AHA EPI-NPAM) 2011 Scientific
Sessions.
54.
Morris CR,
Ansari M, Lavrisha L, Sweeters N, Kuypers F, Vichinsky E. Arginine
therapy: a promising intervention for vaso-occlusive pain episodes in sickle
cell disease. the 6th International
Conference on the Biology, Chemistry, and Therapeutic Applications of Nitric
Oxide. Sakyo-ku,
55.
Morris CR,
Kim H-Y, Trachtenberg F, Wood J, Quinn CT, Sweeters N, Kwiatkowski JL, Thompson
AA, Giardina PJ, Boudreaux J, Olivieri NF, Porter JB, Neufeld EJ, Vichinsky
EP. Risks Factors and Mortality Associated with
Doppler-Defined-Pulmonary Hypertension In Thalassemia
Major: a Report From the Thalassemia Clinical Research Network Longitudinal
Cohort Study. American Thoracic Society International Conference.
56.
Morris CR,
Kuypers F, Hagar RW, Ansari M, Larkin A, Lavrisha L, Wardlaw M, Zheu A, Vichinsky
E, Suh J. Oral glutamine supplementation improves global arginine
bioavailability in patients with sickle cell disease and Doppler-defined
pulmonary hypertension: Preliminary pharmacokinetic results. 5th Annual
Sickle Cell Disease Research and Educational Symposium & Annual National
Sickle Cell Disease Scientific Meeting - Symposium and Scientific Meeting.
57.
Morris CR, Kuypers
F, Hagar RW, Ansari M, Larkin SK, Lavrisha L, Wardlaw M, Zhou A, Vichinsky
E, Suh JH. Metabolic Fate of Oral Glutamine Supplementation within
Plasma and Erythrocytes of Patients with Sickle Cell Disease: Preliminary
Pharmacokinetics Results. American Society of Hematology Annual Meeting.
58.
Morris CR,
Kuypers FA, Hagar RW, Ansari M, Larkin S, Lavrisha L, Zhou A, Vichinsky E,
Suh J. Metabolic Fate Of Oral Glutamine Supplementation Within Plasma And
Erythrocytes Of Patients With Sickle Cell Disease And Pulmonary Hypertension:
Preliminary Pharmacokinetics Results. American Thoracic Society
International Conference.
59.
Morris CR,
Ansari M, Lavrisha L, Sweeters N, Kuypers FA, Vichinsky EP. L-Arginine:
A Promising Nitric Oxide-Based Therapy for Vaso-Occlusive Pain Episodes in
Sickle Cell Disease (SCD). Nitric Oxide Society Sixth
International Conference: Biology, Chemistry, and Therapeutic Applications of
Nitric Oxide.
60.
Nouraie
M, Barst RJ, Rosenzweig EB, Sachdev V, Machado RF, Hassell K, Gibbs JSR, Little
JA, Schraufnagel DE, Krishnamurti L, Novelli EM, Girgis RE, Morris CR,
Badesch DB, Lanzkron S, Castro O, Goldsmith JC, Gladwin M, Gordeuk VR, Kato GJ.
NT-Probnp as a Marker of Cardiopulmonary Compromise and Exercise Limitation In Adults with Sickle Cell Anemia In the Walk-PHaSST Study.
American Society of Hematology Annual Meeting.
61.
Olivieri
NF, Saunthararajah Y, Thayalasuthan V, Kwiatkowski J, Ware RE, Kuypers F,
Kim H-Y, Vichinsky EP. A Pilot Study of Epigenetic-Differentiation
Therapy with Decitabine to Treat Beta-Thalassemia Intermedia. American
Society of Hematology Annual Meeting.
62.
Paulukonis
S, Neumayr L, Coates TD, Vichinsky E, Feuchtbaum L. Emergency
Room Utilization by California Sickle Cell Patients During Pediatric to Adult
Care Transition. American Society of Hematology Annual Meeting.
63.
Powell
B, Feusner J, et al. Adding mercaptopurine and methotrexate to alternate
week ATRA maintenance therapy does not improve the outcome for adults with
Acute Promyelocytic Leukemia (
64.
Rienhoff
HY, Jr, Viprakasit i, Tay LH, Harmatz P, Vichinsky E, Chirnomas
D, Kwiatkowski J, Tapper AE, Porter JB, Neufeld EJ. A Phase 1B
Dose-Escalation Study to Assess the Safety, Tolerability, Pharmacokinetics and
Pharmacodynamics of FBS0701, a Novel Oral Iron Chelator for the Treatment of
Chronic Iron Overload. American Society of Hematology Annual Meeting.
65.
Shenoy
S, Asselin B, Dalal J, Goyal R, Kaufman JL, Loeb D, McCarty J, Robertson K,
Strahlendorf C, Walters MC, Angell J, Huebner D, Shaw PJ. Safety and
Efficacy of Hematopoietic Stem Cell Remobilization with Plerixafor (Mozobil(R))
+ G-CSF In Pediatric Patients with Malignant Disorders.
American Society of Hematology Annual Meeting.
66.
Shepherd
JA, Fan B, Lu Y, Marquez L, Salama K, Hwang J, Fung EB. DXA with
serum ferritin predicts liver iron concentration and change in concentration
better than ferritin alone. International Society for Clinical
Densitometry Annual Meeting.
67.
Simon
SI, Chase S, Larkin SK, Kuypers F, Styles L, Wun T, Thackray H, Magnani
JL. Effects of Selectin Antagonist GMI-1070 on the
68.
Singer ST, Kuypers
F, Fineman J, Larkin SK, Jeng M, Harmon C, Sweeters N, Higa A, Vichinsky
E. The Effect of Thalassemia and Other
69.
Thompson
A, Kim H, Calamaras D, Beatty J, Singer ST, Vichinsky E,
Braunstein J, Yamashita R, Giardina P, Olivieri N, Parmar N, Trachtenberg F,
Neufeld E, Kwiatkowski J. Thalassemia Clinical Research Network. Pregnancy
outcomes in women with thalassemia in North America and the UK. 12th
International Conference on Thalassemia.
70.
Treadwell M,
Barreda F, Major K, Walker V, Payton W, Kaur K, Vichinsky E. Mental
Health Symptoms, Quality of Life and Barriers to Accessing Health Care in
Sickle Cell Disease. The 53rd Annual Meeting of the American Society of
Hematology.
71.
Treadwell M,
Levine RE, Keller SD, Hassell K, Werner E. Understanding perspectives of
adults with sickle cell disease in developing a disease-specific quality of
life measurement system. International Society for Quality of Life
Research17th Annual Conference.
72.
Vichinsky E,
Bernaudin F, Forni GL, Gardner R, Hassell K, Heeney MM, Inusa B, Kutlar A, Lane
PA, Mathias L, Porter JB, Tebbi CK, Wilson FL, Griffel L, Deng W, Giannone V,
Coates TD. Long-Term Safety and Efficacy of Deferasirox (Exjade(R)) In
Transfused Patients with Sickle Cell Disease Treated for up to 5 Years. American
Society of Hematology Annual Meeting.
73.
Vichinsky E,
Chu J, Walters M, Lal A, Singer ST, Foote D, Shiota S. Successful
Hematopoietic Cell Transplantation for Alpha Thalassemia Major. American
Society of Pediatric Hematology Oncology.
74.
Vichinsky E,
Neumayr L, Gold JI, Weiner MW, Kasten J, Truran D, Snyder C, Kesler K,
Hussein AM, Harrington TJ, McMahon L, Gordeuk VR, Kutlar A, Orringer EP, De
Castro LM, Field J, Swerdlow PS, Bessman JD, Snyder R, Strouse JJ, Armstrong FD.
A Randomized Trial of the Safety and Benefit of Transfusion Vs. Standard
Care In the Prevention of Sickle Cell-Related Complications In Adults: a
Preliminary Report From the Phase II NHLBI Comprehensive Sickle Cell Centers (
75.
Vichinsky E,
Torres M, Glass J, Minniti C, Barrette S, Habr D, Lynch N, Yiyun Z, Files B. A
Randomized Phase II Study Evaluating the Efficacy and Safety of Deferasirox
Versus Deferoxamine in Patients with Sickle Cell Disease (SCD): 2-Year Results
Including Pharmacokinetics (PK) and Safety of Deferasirox with Concomitant
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date revised: